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Leibniz's lifelong devotion to the idea of the characteristica universalis found its starting point in his early work Dissertatio De Ars Combinаtorica. Already there the conceptualization of sign notion plays a fundamental role in his entire scientific and philosophic thought. While left unfinished, this project produced a crop of important results in the various fields of knowledge, which, like an Ariadne’s thread, trace paths in the maze of sign-related topics in Leibniz’s legacy. There belong sign combination rules or combinatorics, including binary calculus; definition of sign and its place in the process of cognition; the problem of primary irreducible notions and their alphabet; ars memoriae (mnemonics) and the theory of cognitio caeca (blind cognition); etc.